Complement C1s
Synonyms
C 1 Esterase
C1 Esterase
C1s Complement
C1s, Complement
Complement 1 Esterase
Complement 1s
Complement Component 1s
Complement, C1s
Component 1s, Complement
Esterase, C 1
Esterase, C1
Esterase, Complement 1
A 77-kDa subcomponent of complement C1, encoded by gene C1S, is a SERINE PROTEASE existing as a proenzyme (homodimer) in the intact complement C1 complex. Upon the binding of COMPLEMENT C1Q to antibodies, the activated COMPLEMENT C1R cleaves C1s into two chains, A (heavy) and B (light, the serine protease), linked by disulfide bonds yielding the active C1s. The activated C1s, in turn, cleaves COMPLEMENT C2 and COMPLEMENT C4 to form C4b2a (CLASSICAL C3 CONVERTASE).