Histidine Ammonia-Lyase

Synonyms

Ammonia-Lyase, Histidine

Deaminase, Histidine

Histidase

Histidinase

Histidine Ammonia Lyase

Histidine Deaminase

Histidine alpha Deaminase

Histidine alpha-Deaminase

L-Histidine ammonia-lyase

alpha-Deaminase, Histidine

An enzyme that catalyzes the first step of histidine catabolism, forming UROCANIC ACID and AMMONIA from HISTIDINE. Deficiency of this enzyme is associated with elevated levels of serum histidine and is called histidinemia (AMINO ACID METABOLISM, INBORN ERRORS).