Ichthyosiform Erythroderma, Congenital
Synonyms
Congenital Ichthyosiform Erythroderma
Congenital Ichthyosiform Erythroderma, Dry Type
Congenital Ichthyosiform Erythroderma, Wet Type
Congenital Ichthyosiform Erythrodermas
Erythroderma, Congenital Ichthyosiform
Erythrodermas, Congenital Ichthyosiform
Ichthyosiform Erythrodermas, Congenital
Designation for several severe forms of ichthyosis, present at birth, that are characterized by hyperkeratotic scaling. Infants may be born encased in a collodion membrane which begins shedding within 24 hours. This is followed in about two weeks by persistent generalized scaling. The forms include bullous (HYPERKERATOSIS, EPIDERMOLYTIC), non-bullous (ICHTHYOSIS, LAMELLAR), wet type, and dry type.