Moyamoya Disease
Synonyms
Cerebrovascular Moyamoya Disease
Classic Moyamoya Disease
Disease, Classic Moyamoya
Disease, Moya-Moya
Disease, Primary Moyamoya
Moya Moya Disease
Moya-Moya Disease
Moyamoya Disease, Classic
Moyamoya Disease, Primary
Moyamoya Disease, Secondary
Moyamoya Diseases, Primary
Moyamoya Syndrome
Primary Moyamoya Disease
Primary Moyamoya Diseases
Progressive Intracranial Occlusive Arteropathy (Moyamoya)
Secondary Moyamoya Disease
A noninflammatory, progressive occlusion of the intracranial CAROTID ARTERIES and the formation of netlike collateral arteries arising from the CIRCLE OF WILLIS. Cerebral angiogram shows the puff-of-smoke (moyamoya) collaterals at the base of the brain. It is characterized by endothelial HYPERPLASIA and FIBROSIS with thickening of arterial walls. This disease primarily affects children but can also occur in adults.