Olivopontocerebellar Atrophies
Synonyms
Ataxia, Presenile
Ataxias, Presenile
Atrophy, Familial Olivopontocerebellar
Atrophy, Idiopathic Olivopontocerebellar
Atrophy, Inherited Olivopontocerebellar
Atrophy, Nonfamilial Olivopontocerebellar
Atrophy, Olivo-Ponto-Cerebellar
Atrophy, Olivopontocerebellar
Atrophy, Pontoolivocerebellar
Degeneration, Olivo-Ponto-Cerebellar
Degeneration, Olivopontocerebellar
Degenerations, Olivo-Ponto-Cerebellar
Degenerations, Olivopontocerebellar
Dejerine Thomas Syndrome
Dejerine-Thomas Syndrome
Familial Olivopontocerebellar Atrophies
Familial Olivopontocerebellar Atrophy
Idiopathic Olivopontocerebellar Atrophies
Idiopathic Olivopontocerebellar Atrophy
Inherited Olivopontocerebellar Atrophies
Inherited Olivopontocerebellar Atrophy
Nonfamilial Olivopontocerebellar Atrophies
Nonfamilial Olivopontocerebellar Atrophy
Olivo Ponto Cerebellar Atrophy
Olivo Ponto Cerebellar Degeneration
Olivo-Ponto-Cerebellar Atrophy
Olivo-Ponto-Cerebellar Degeneration
Olivo-Ponto-Cerebellar Degenerations
Olivopontocerebellar Atrophies, Familial
Olivopontocerebellar Atrophies, Idiopathic
Olivopontocerebellar Atrophies, Inherited
Olivopontocerebellar Atrophies, Nonfamilial
Olivopontocerebellar Atrophy
Olivopontocerebellar Atrophy, Familial
Olivopontocerebellar Atrophy, Idiopathic
Olivopontocerebellar Atrophy, Inherited
Olivopontocerebellar Atrophy, Nonfamilial
Olivopontocerebellar Degeneration
Olivopontocerebellar Degenerations
Pontoolivocerebellar Atrophies
Pontoolivocerebellar Atrophy
Presenile Ataxia
Presenile Ataxias
Syndrome, Dejerine-Thomas
A group of inherited and sporadic disorders which share progressive ataxia in combination with atrophy of the CEREBELLUM; PONS; and inferior olivary nuclei. Additional clinical features may include MUSCLE RIGIDITY; NYSTAGMUS, PATHOLOGIC; RETINAL DEGENERATION; MUSCLE SPASTICITY; DEMENTIA; URINARY INCONTINENCE; and OPHTHALMOPLEGIA. The familial form has an earlier onset (second decade) and may feature spinal cord atrophy. The sporadic form tends to present in the fifth or sixth decade, and is considered a clinical subtype of MULTIPLE SYSTEM ATROPHY. (From Adams et al., Principles of Neurology, 6th ed, p1085)
See Also