Persistent Fetal Circulation Syndrome
Synonyms
ACD MPV
ACD-MPV
ACDMPV
Alveolar Capillary Dysplasia With Misalignment Of Pulmonary Veins
Alveolar Capillary Dysplasia With Misalignment Of Pulmonary Veins And Other Congenital Anomalies
Circulation, Persistent Fetal
Familial Persistent Pulmonary Hypertension of the Newborn
Fetal Circulation, Persistent
Hypertension, Pulmonary, of Newborn, Persistent
Misalignment of the Pulmonary Vessels
Persistent Fetal Circulation
Persistent Pulmonary Hypertension of Newborn
Pulmonary Hypertension, Familial Persistent, of the Newborn
A syndrome of persistent PULMONARY HYPERTENSION in the newborn infant (INFANT, NEWBORN) without demonstrable HEART DISEASES. This neonatal condition can be caused by severe pulmonary vasoconstriction (reactive type), hypertrophy of pulmonary arterial muscle (hypertrophic type), or abnormally developed pulmonary arterioles (hypoplastic type). The newborn patient exhibits CYANOSIS and ACIDOSIS due to the persistence of fetal circulatory pattern of right-to-left shunting of blood through a patent ductus arteriosus (DUCTUS ARTERIOSUS, PATENT) and at times a patent foramen ovale (FORAMEN OVALE, PATENT).
See Also