Phenylalanine Hydroxylase
Synonyms
4-Hydroxylase, Phenylalanine
4-Monooxygenase, Phenylalanine
Hydroxylase, Phenylalanine
L-Phenylalanine,tetrahydrobiopterin:oxygen oxidoreductase (4-hydroxylating)
Phenylalanine 4 Hydroxylase
Phenylalanine 4 Monooxygenase
Phenylalanine 4-Hydroxylase
Phenylalanine 4-Monooxygenase
An enzyme of the oxidoreductase class that catalyzes the formation of L-TYROSINE, dihydrobiopterin, and water from L-PHENYLALANINE, tetrahydrobiopterin, and oxygen. Deficiency of this enzyme may cause PHENYLKETONURIAS and PHENYLKETONURIA, MATERNAL. EC 1.14.16.1.