Purpura, Thrombotic Thrombocytopenic
Synonyms
Congenital Thrombotic Thrombocytopenic Purpura
Disease, Moschcowitz
Disease, Moschkowitz
Familial Thrombotic Microangiopathy
Familial Thrombotic Thrombocytopenia Purpura
Familial Thrombotic Thrombocytopenic Purpura
Microangiopathic Hemolytic Anemia, Congenital
Microangiopathy, Familial Thrombotic
Moschcowitz Disease
Moschkowitz Disease
Purpura, Thrombotic Thrombopenic
Schulman Upshaw Syndrome
Schulman-Upshaw Syndrome
Syndrome, Schulman-Upshaw
Syndrome, Upshaw-Schulman
Thrombocytopenic Purpura, Thrombotic
Thrombopenic Purpura, Thrombotic
Thrombotic Microangiopathy, Familial
Thrombotic Thrombocytopenic Purpura
Thrombotic Thrombocytopenic Purpura, Congenital
Thrombotic Thrombocytopenic Purpura, Familial
Thrombotic Thrombopenic Purpura
Upshaw Factor, Deficiency of
Upshaw Schulman Syndrome
Upshaw-Schulman Syndrome
An acquired, congenital, or familial disorder caused by PLATELET AGGREGATION with THROMBOSIS in terminal arterioles and capillaries. Clinical features include THROMBOCYTOPENIA; HEMOLYTIC ANEMIA; AZOTEMIA; FEVER; and thrombotic microangiopathy. The classical form also includes neurological symptoms and end-organ damage, such as RENAL FAILURE.