Smith-Lemli-Opitz Syndrome
Synonyms
7-Dehydrocholesterol Reductase Deficiencies
7-Dehydrocholesterol Reductase Deficiency
Acrodysgenital Syndrome, Lethal
Acrodysgenital Syndromes, Lethal
Deficiencies, 7-Dehydrocholesterol Reductase
Deficiency, 7-Dehydrocholesterol Reductase
Hyperotosis Corticalis Generalisata Familiaris
Lethal Acrodysgenital Syndrome
Lethal Acrodysgenital Syndromes
Polydactyly, Sex Reversal, Renal Hypoplasia, And Unilobar Lung
RSH SLO Syndrome
RSH Syndrome
RSH Syndromes
RSH-SLO Syndrome
RSH-SLO Syndromes
Reductase Deficiencies, 7-Dehydrocholesterol
Reductase Deficiency, 7-Dehydrocholesterol
Rutledge Friedman Harrod Syndrome
Rutledge Lethal Multiple Congenital Anomaly Syndrome
SLO Syndrome
SLO Syndromes
Smith Lemli Opitz Syndrome
Smith Lemli Opitz Syndrome, Type 2
Smith Lemli Opitz Syndrome, Type I
Smith Lemli Opitz Syndrome, Type II
Smith Lemli Opitz syndrome, type 1
Smith-Lemli-Opitz Syndrome, Type 1
Smith-Lemli-Opitz Syndrome, Type 2
Smith-Lemli-Opitz Syndrome, Type I
Smith-Lemli-Opitz Syndrome, Type II
Syndrome, Lethal Acrodysgenital
Syndrome, RSH
Syndrome, SLO
Syndromes, RSH
Syndromes, SLO
An autosomal recessive disorder of CHOLESTEROL metabolism. It is caused by a deficiency of 7-dehydrocholesterol reductase, the enzyme that converts 7-dehydrocholesterol to cholesterol, leading to an abnormally low plasma cholesterol. This syndrome is characterized by multiple CONGENITAL ABNORMALITIES, growth deficiency, and INTELLECTUAL DISABILITY.