Caroli Disease
Synonyms
Caroli Syndrome
Caroli's Disease
Caroli's Syndrome
Carolis Disease
Carolis Syndrome
Disease, Caroli
Disease, Caroli's
Syndrome, Caroli's
Congenital cystic dilatation of the intrahepatic bile ducts (BILE DUCTS, INTRAHEPATIC). It consists of 2 types: simple Caroli disease is characterized by bile duct dilatation (ectasia) alone; and complex Caroli disease is characterized by bile duct dilatation with extensive hepatic fibrosis and portal hypertension (HYPERTENSION, PORTAL). Benign renal tubular ectasia is associated with both types of Caroli disease.