Erythrokeratodermia Variabilis
Synonyms
Erythro et Keratodermia Variabilis
Erythrokeratodermia Figurata Variabilis
Erythrokeratodermia Figurata, Congenital Familial, in Plaqus
Erythrokeratodermia Variabilis with Erythema Gyratum Repens
Erythrokeratodermia, Progressive Symmetric
Greither Disease
Mendes De Costa Syndrome
Progressive Symmetric Erythrokeratodermia
Transgrediens et Progrediens Palmoplantar Keratoderma
An autosomal dominant skin disease characterized by transient and variable noninflammatory ERYTHEMA and hyperkeratosis. It has been associated with mutations in the genes that code for CONNEXINS. Erythrokeratodermia variabilis inherited in an autosomal recessive fashion has also been reported. Affected individuals often develop PALMOPLANTAR KERATODERMA.