Glutaryl-CoA Dehydrogenase

Synonyms

CoA Dehydrogenase, Glutaryl

Dehydrogenase, Glutaryl CoA

Dehydrogenase, Glutaryl-CoA

Dehydrogenase, Glutaryl-Coenzyme A

Glutaryl CoA Dehydrogenase

Glutaryl Coenzyme A Dehydrogenase

Glutaryl-Coenzyme A Dehydrogenase

A flavoprotein enzyme that is responsible for the catabolism of LYSINE; HYDROXYLYSINE; and TRYPTOPHAN. It catalyzes the oxidation of GLUTARYL-CoA to crotonoyl-CoA using FAD as a cofactor. Glutaric aciduria type I is an inborn error of metabolism due to the deficiency of glutaryl-CoA dehydrogenase.