Holoprosencephaly
Synonyms
Alobar Holoprosencephalies
Alobar Holoprosencephaly
Arhinencephalies
Arhinencephaly
Holoprosencephalies
Holoprosencephalies, Alobar
Holoprosencephalies, Lobar
Holoprosencephalies, Semilobar
Holoprosencephaly, Alobar
Holoprosencephaly, Familial Alobar
Holoprosencephaly, Lobar
Holoprosencephaly, Semilobar
Lobar Holoprosencephalies
Lobar Holoprosencephaly
Semilobar Holoprosencephalies
Semilobar Holoprosencephaly
Anterior midline brain, cranial, and facial malformations resulting from the failure of the embryonic prosencephalon to undergo segmentation and cleavage. Alobar prosencephaly is the most severe form and features anophthalmia; cyclopia; severe INTELLECTUAL DISABILITY; CLEFT LIP; CLEFT PALATE; SEIZURES; and microcephaly. Semilobar holoprosencepaly is characterized by hypotelorism, microphthalmia, coloboma, nasal malformations, and variable degrees of INTELLECTUAL DISABILITY. Lobar holoprosencephaly is associated with mild (or absent) facial malformations and intellectual abilities that range from mild INTELLECTUAL DISABILITY to normal. Holoprosencephaly is associated with CHROMOSOME ABNORMALITIES.