Ovotesticular Disorders of Sex Development

Synonyms

46,XX Gonadal Dysgenesis, Complete, Sry-Positive

46,XX True Hermaphroditism, Sry-Positive

DSD, Ovotesticular

DSDs, Ovotesticular

Familial True Hermaphroditism

Familial True Hermaphroditisms

Familial XX True Hermaphroditism

Hermaphroditism, Familial True

Hermaphroditism, True

Hermaphroditisms, Familial True

Hermaphroditisms, True

Ovotesticular DSD

Ovotesticular DSDs

Ovotesticular Disorder Of Sex Development

True Hermaphroditism

True Hermaphroditism, Familial

True Hermaphroditisms

True Hermaphroditisms, Familial

XX Male Syndrome, Sry Positive

XX Male Syndrome, Sry-Positive

Conditions of sexual ambiguity in which the individual possesses gonadal tissues of both sexes, tissues from the OVARY and the TESTIS. There can be a testis on one side and an ovary on the other (lateral), or there may be combined ovarian and testicular tissue (ovotestes) on each side (bilateral). The karyotype may be 46,XX; 46,XY; or a mosaic of 46,XX/46,XY. These disorders have historically been called true hermaphroditism.