Scimitar Syndrome

Synonyms

Anomalous Pulmonary Venous Return

Anomaly, Scimitar

Pulmonary Venous Return Anomaly

Scimitar Anomaly

Syndrome, Scimitar

TAPVR

TAPVR1

Total Anomalous Pulmonary Venous Return

Total Anomalous Pulmonary Venous Return 1

An anomalous pulmonary venous return in which the right PULMONARY VEIN is not connected to the LEFT ATRIUM but to the INFERIOR VENA CAVA. Scimitar syndrome is named for the crescent- or Turkish sword-like shadow in the chest radiography and is often associated with hypoplasia of the right lung and right pulmonary artery, and dextroposition of the heart.